Prevalence & features of inner ear malformations among children with congenital sensorineural hearing loss: A Public Cochlear Implant Centre Experience

  • Jawwad Ahmed, Dr. Capital Hospital PGMI, CDA Islamabad
  • Ghulam Saqulain, Dr. Capital Hospital PGMI, CDA Islamabad https://orcid.org/0000-0002-6452-9339
  • Muhammad Iqbal javed Khan, Dr. Bradford Teaching Hospitals NHS Foundation Trust, England
  • Mobeen Kausar, Dr. DHQ Hospital, Rawalpindi
Keywords: Computed tomography scan, Middle ear malformations, Prevalence

Abstract

Objective: To determine the prevalence and features of inner ear anomalies in children with congenital profound hearing loss who presented at our cochlear implant center based on imaging studies.

Methods: This retrospective study reviewed charts of children with congenital SNHL, who presented to Department of Otolaryngology & Auditory Implant Centre, Capital Hospital Islamabad over a period of 2 years from 1st May 2017 to 30th April 2019. These included 481 cases of both genders aged between 1 to 12 years. After gathering demographic data, audiological data, computed tomography findings of the temporal bone were analyzed. Data was analyzed using SPSS 22.

Results: The Inner Ear Malformations were identified in 48(10%) children including 28 (58.33%) males and 20 (41.67%) female. Most 20(41.67%) presented at >3-5 years of age followed by 19(39.58%) at 2-3 years. However, no significant association of gender (p=0.57, p=0.076) and age of presentation (p=0.344, p=0.697) for right and left ears was noted with inner ear malformations. The most common anomaly noted were CLA, CH-III and CH-II in decreasing order of frequency in both ears.

Conclusion: The prevalence of IEM’s was found to be 48(10%). Commonest anomalies noted were CLA, CH-III and CH-II. No significant association of gender and age of presentation was noted with type of anomaly in both ears.

doi: https://doi.org/10.12669/pjms.36.7.3134

How to cite this:
Ahmed J, Saqulain G, Khan MIJ, Kausar M. Prevalence & features of inner ear malformations among children with congenital sensorineural hearing loss: A Public Cochlear Implant Centre Experience . Pak J Med Sci. 2020;36(7):1511-1516.  doi: https://doi.org/10.12669/pjms.36.7.3134

This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Author Biographies

Jawwad Ahmed, Dr., Capital Hospital PGMI, CDA Islamabad

Dr. Jawwad Ahmed, F.C.P.S
Associate Surgeon Otolaryngology Department
Capital Hospital, Islamabad, Pakistan
drjawwad@hotmail.com

Ghulam Saqulain, Dr., Capital Hospital PGMI, CDA Islamabad

Dr. Ghulam Saqulain, D.L.O, F.C.P.S
Head of Department of Otorhinolaryngology
Capital Hospital PGMI, CDA, Islamabad, Pakistan
E-mail: ghulam_saqulain@yahoo.com

Muhammad Iqbal javed Khan, Dr., Bradford Teaching Hospitals NHS Foundation Trust, England

Dr. Mumammad Iqbal Javed Khan, FRCS
Consultant Otologist and Skull Base Surgeon
Bradford Teaching Hospitals NHS Foundation Trust
E-mail: mijkhan@yahoo.com

 

Mobeen Kausar, Dr., DHQ Hospital, Rawalpindi

Dr. Mobeen Kausar, MPH
Deputy Medical Superintendent,
Healthcare Commission Coordinator
DHQ Hospital, Rawalpindi
Email: drmobeenj@gmail.com

Published
2020-10-17
How to Cite
Ahmed, J., Saqulain, G., Khan, M., & Kausar, M. (2020). Prevalence & features of inner ear malformations among children with congenital sensorineural hearing loss: A Public Cochlear Implant Centre Experience. Pakistan Journal of Medical Sciences, 36(7). https://doi.org/10.12669/pjms.36.7.3134
Section
Original Articles